Does Osteogenesis imperfecta lead to a Hearing loss?

According to a survey on the hearing loss in osteogenesis imperfecta, more than 50 percent of people who have osteogenesis imperfecta have hearing loss. Osteogenesis imperfecta(OI), most common heritable disorder of the bone associated with increased joint bone mobility, minor injury, and deafness.
Yes, osteogenesis imperfecta lead to hearing impairment but not every person who has OI develops a loss of hearing. The incidence of OI is much higher than in the general population.
In OI sometimes the cause is unknown. Sometimes is due to visible deformities in inner ear and ossicles may lead to deafness. It is important to how osteogenesis imperfecta leads to hearing loss.

Why hearing loss causes due to Osteogenesis
The reason why the hearing causes due to osteogenesis imperfecta is not definitely known. Patients suffering from OI have a greater chance of skull fracture which is associated with the hearing loss. Footplate fixation is one of the reasons for the conductive hearing loss in the OI.

How Osteogenesis imperfecta lead to hearing loss
Osteogenesis imperfecta is due to mutation including several genes. A phenotype or genotype connected to hearing loss has not been established in OI. There are various environmental factors that contribute to the hearing problem in people with OI. These factors include noise, infection and head injury.
The loss of hearing generally starts at any age but with people who have osteogenesis imperfecta, hearing loss in those people starts at an early stage and increases with time.
Hearing impairment in osteogenesis imperfecta can be a conductive hearing loss, sensorineural hearing loss,mixed hearing loss depending on the symptoms.
Consult an audiologist for your hearing problem. He will recommend a hearing test. Your hearing test will decide the treatment of the hearing loss. The treatment can be hearing aid or cochlear implants depending on the type of hearing loss.


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